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Case Report
Rare Combination of Biventricular Non-Compaction Cardiomyopathy and a Circumflex Coronary Artery-To-Pulmonary Artery Fistula
Author(s): Sana Fennira*, Yassmine Kammoun, Mohamed AliTekaya, Hela Sarray, Sofien Kamoun, and Sondos Kraiem
Abstract:
Non-compaction cardiomyopathy is a rare congenital disease resulting from the cessation of normal embryogenesis of the myocardium that may be exceptionally associated to coronary fistulae. Its main feature is the existence of many deep ventricular trabeculations generally located in the left ventricle. Diagnosis is based on echocardiography and Magnetic Resonance Imaging (MRI). To our knowledge, this is the first case reported of the association of biventricular non-compaction and a circumflex coronary artery-to-pulmonary artery fistula. The interest of this case lies in its rarity and its therapeutic implications.
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Case Report
Neurological Manifestations Probably Secondary to Iron Deposits in the CNS in Patients with Myelodysplastic Syndrome
Author(s): Ana Flávia Dinardi Alves Pinto*, Vanessa Afonso Silva Pardi, Ludmila Emily Jesus Paula, Debora Rosa Portilho, Sândala Cristina Fernandes Silveira and Leonardo Rodrigues de Oliveira
Abstract:
Myelodysplastic syndromes consist of a cluster of clonal hematopoietic diseases characterized by ineffective hematopoiesis, bone marrow dysplasia, cytopenias in peripheral blood, and elevated risk of transformation to acute myeloid leukemia. Patients with myelodysplastic syndromes who undergo regular and chronic transfusion regimen of red blood cells for management of symptomatic anemia may develop organ dysfunction associated with iron overload such as hepatic, cardiac and endocrine dysfunction. In this report, it was described a patient with myelodysplastic syndrome with refractory cytopenias with multilinear dysplasia and transfusion iron overload, who evolved with ataxia, recurrent vomiting and increased dependence on daily life activities. Magnetic resonance imaging of the brain revealed iron deposits in the dentate nucleus of cerebellum and basal ganglia, with a likely relationship between iron deposition in the central nervous system and the observed neurological dysfunctions. There are few cases reported in the literature of iron deposits in the central nervous system causing neurological manifestations. However, once iron overload is established, attention should be directed to possible deposits of the metal to determine neurological dysfunction.
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Case Report
Isorythmic Dissociation by Alternating Interference with Double Nodal Response after Cardiac Surgery
Author(s): Sana Fennira*, Sofien Kamoun, Yassmine Kammoun, Boutayna Besbes, NazihaTurki and Sondes Kraiem
Abstract:
Isorythmic atrioventricular dissociation by interference is a rhythmic entity that is rare in current practice and often unrecognized. Its association with a nodal duality generating a double ventricular response is exceptional.We report the observation of such association in a postoperative context of a surgical correction of interauricular communication following an attempt to close this defect by an amplatzer complicated by a migration of the prosthesis.
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